Hepatocellular carcinoma in ADA-SCID patient after hematopoietic stem cell transplantation

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dc.contributor.authorUçku, Duygu
dc.contributor.authorArmutlu, Ayşe
dc.contributor.authorÇipe, Funda
dc.contributor.authorZengin Ersoy, Gizem
dc.contributor.authorKarakaya, Afak Durur
dc.contributor.authorArıkan, Çiğdem
dc.date.accessioned2023-04-14T05:56:16Z
dc.date.available2023-04-14T05:56:16Z
dc.date.issued2023en_US
dc.departmentFakülteler, Tıp Fakültesi, Dahili Tıp Bilimleri Bölümü, Çocuk Sağlığı ve Hastalıkları Ana Bilim Dalıen_US
dc.description.abstractAdenosine deaminase (ADA) deficiency is one of the most prevalent forms of severe combined immunodeficiency and results in the accumulation of toxic substrates which creates a systemic metabolic disease. It predisposes patients to the development of malignancies, most commonly lymphoma. We report an 8-month-old infant with ADA deficient severe combined immunodeficiency who developed progressive liver dysfunction and hepatocellular carcinoma after successful hematopoietic stem cell transplantation. This is the first case report of an ADA-deficient patient who presented with hepatocellular carcinoma and gives an insight into the complex etiology that can lie behind liver dysfunction in these patients.en_US
dc.identifier.citationUçku, D., Armutlu, A., Çipe, F., Zengin Ersoy, G., Karakaya, A. D., Arıkan, Ç. (2023). Hepatocellular carcinoma in ADA-SCID patient after hematopoietic stem cell transplantation. Journal of Pediatric Hematology/Oncology, 45(5), pp. 285-289.en_US
dc.identifier.endpage289en_US
dc.identifier.issn1077-4114
dc.identifier.issn1536-3678
dc.identifier.issue5en_US
dc.identifier.scopus2-s2.0-85163807628
dc.identifier.scopusqualityQ3
dc.identifier.startpage285en_US
dc.identifier.urihttps://hdl.handle.net/20.500.12939/3469
dc.identifier.volume45en_US
dc.identifier.wosWOS:001017782300012
dc.identifier.wosqualityQ3
dc.indekslendigikaynakWeb of Science
dc.indekslendigikaynakScopus
dc.indekslendigikaynakPubMed
dc.institutionauthorZengin Ersoy, Gizem
dc.language.isoen
dc.relation.ispartofJournal of Pediatric Hematology/Oncology
dc.relation.isversionof10.1097/MPH.0000000000002661en_US
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanıen_US
dc.rightsinfo:eu-repo/semantics/closedAccessen_US
dc.subjectAdenosine Deaminaseen_US
dc.subjectSevere Combined Immunodeficiencyen_US
dc.subjectHematopoietic Stem Cell Transplantationen_US
dc.subjectHepatocellular Carcinomaen_US
dc.subjectLiver Transplantationen_US
dc.titleHepatocellular carcinoma in ADA-SCID patient after hematopoietic stem cell transplantation
dc.typeArticle

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